Home PageAbout the FoundationCurrent NewsletterContact UsSite MapShopping CartAccount Login
  
 

Some questions to the groups of Geneticists who are working on Joubert Syndrome answers from the University of San Diego
by Dr. Joseph Gleeson

Oct 15, 2003

Hi Everyone:

In response to some questions that some members had regarding the scientists, collaboration and a recent new publications for another mutation being discovered, I sent some questions to the groups of Geneticists who are working on Joubert Syndrome. The responses below are from the San Diego group.

Cheryl Duquette, President and Co-Founder
Joubert Syndrome Foundation & Related Cerebellar Disorders
6931 South Carlinda Ave.
Columbia, MD 21046
410-997-8084 fax: 410-992-9184
email: joubertduquette@comcast.net

Dr. Joseph Gleeson's response:

Cheryl Duquette asked me to answer some questions regarding the state of collaborations between the different laboratories working on Joubert syndrome, especially in reference to the relationship between my group and the University of Washington team, which includes Drs. Chance and Parissi. We very much respect your willingness to participate in these studies, and I view it as my duty to answer your questions here in as open a manner as possible.

First, let me thank you all for your willingness to participate with genetic studies. Our work on JS really depends on your participation, and our goal is the same as yours: improved pre-diagnosis, prenatal testing and ultimately treatment, so that this research is beneficial to individuals with JS and families. We believe our recent publication on JS to be a major advance in our understanding of the genetic causes of this condition. I will briefly summarize the findings:

We identified the first solid genetic evidence that the atypical form of JS (that includes eye or kidney disease) is distinct from the form that does not include these features. In our publication, we report finding three families that show genetic "linkage" to a place on chromosome 11. This means that there is a region on chromosome 11 that contains a gene that, when mutated, causes this form of JS. We have not identified the actual gene yet, but we are working hard to do this in collaboration with several research groups.

We have now found several families (we believe about 10) that show possible evidence for disease on chromosome 11. We cannot be absolutely certain regarding about 5 of these families, because they are relatively small and our technique works best on large families. In these families, where Joubert syndrome can be clearly “linked” to chromosome 11, prenatal testing should now be possible.

Joubert Syndrome Foundation (JSF) Question: Are Dr. Chance and Dr. Gleeson working together or separately on the genetic studies?

Joseph Gleeson MD. (JG) Answer: Unfortunately, Dr. Chance's group and my group are not working together at the present time on gene
identification in JS.

JSF Question: If we sent blood to Dr. Chance, may we also want to send to Dr. Gleeson?

JG Answer: It is certainly true that the more DNA samples we have to work with, the faster our research will progress. Although it is not ideal to have blood drawn more than once, members of the JSF should know that samples are not being universally shared. For example, with a few exceptions, my lab is not exchanging samples with the laboratory at the University of Washington.

Since different research groups are obtaining different results, and are using different strategies in searching for the genes, I think parents who have sent samples to other laboratories should strongly consider enrolling in the Gleeson Lab study, and any other studies that were making advances.

Although we are not collaborating currently, I hope that we can collaborate in the future. The University of Washington group headed by Dr. Chance has done important work on Joubert syndrome, and we encourage you to participate in studies with the knowledge that researchers using a with a diversity of approaches will lead to the swiftest progress.

Thank you very much,

Yours sincerely,

Joseph Gleeson, MD
Pediatric Neurology
jogleeson@ucsd.edu
http://gleesongenetics.ucsd.edu
Ph 858-822-3786 Fax 858-534-1437
Toll free: 1-866-KID-MIND (866-543-6463)

Back to Physician Research & Articles

 

The views expressed do not necessarily reflect those of the donors. The articles, announcements, and resources included on this website are for information only and should not be considered as medical advice. Please always consult your physician for medical advice. The Joubert Syndrome Foundation & Related Cerebellar Disorders does not endorse any product, service, or theory referred to on the website.
 

© 1992-2009 Joubert Foundation All rights reserved. Terms of Use and Disclaimer
Web Design & Hosting Provided by Webtrix

Joubert Foundation Tag Cloud
arima  cerebellar  cerebellum  coach  dekaban  disease  hypoplasia  joubert  prognosis  research  senior-loken  syndrome  treatment  varadi